Erschienen in:
11.05.2024 | Letter to the Editor
Autonomic neuropathy improving after intravenous immunoglobulin therapy
verfasst von:
Claudia Alberti, Jacopo Spagliardi, Franca Barbic, Pietro Emiliano Doneddu, Claudia Cutellè, Raffaello Furlan, Eduardo Nobile-Orazio.
Erschienen in:
Clinical Autonomic Research
|
Ausgabe 2/2024
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Excerpt
Autoimmune autonomic neuropathies (AANs) represent peripheral neuropathies marked by immune-mediated autonomic symptoms. Traditionally, autoimmune autonomic ganglionopathy (AAG) was defined by ganglionic acetylcholine receptor (gAchR) antibody positivity [
1]. Recent cases include seronegative AAN and limited forms of presumed autoimmune autonomic failure [
1‐
4]. Diagnosis necessitates clinical suspicion due to the absence of a specific dysimmunity biomarker. Immunomodulating therapies have shown efficacy in autonomic neuropathies, including Sjögren’s disease and paraneoplastic conditions [
1,
5]. …